TY - JOUR ID - TI - Macrophage Activation Syndrome in a Child with Systemic Juvenile Rheumatoid Arthritis AU - Ali M. Al- Yasry AU - Jalal A. Ashoor AU - Intisar H. Al- Kurdi AU - Sabah N. Al-Musawi AU - Zuhair M. Al-Musawi PY - 2007 VL - 1 no.2 IS - 1 SP - 170 EP - 173 JO - Karbala Journal of Medicine مجلة كربلاء الطبية SN - 19905483 29580889 AB - Macrophage activation syndrome (MAS) is a rare and potentially fatal complication of rheumaticdisorders in children; we describe a 14-month old boy in whom MAS developed as first presentation ofsystemic juvenile rheumatoid arthritis (S-JRA). He suffered from fever, bleeding tendency from mouth,gastro-intestinal tract, ecchymosis & site of injections followed by bilateral wrist swellings. Physicalexamination revealed cervical lymphadenopathy & hepatosplenomegaly. Laboratory findings wereabnormal liver enzymes, coagulopathies resembling disseminated intravascular coagulation, anemia,thrombocytopenia and abnormal C.S.F. findings.Up to the best of my knowledge this could be the first MAS associated with S-JRA in Iraq.Key words: Macrophage Activation Syndrome, Arthritis, Juvenile Rheumatoid

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